Mondini（1791）首次报道一例先天性内耳畸形，其后众多学者报道了多种先天性内耳畸形，如被后来学者们经常引用的Mondini和Michel畸形，但也常有错误的引用。为使描述上保持一致，作者对其作一简要回顾。Mondini对一名先天性全聋，而死于意外的8岁男孩的颧骨进行了令人信服的 Mondini (1791) first reported a case of congenital deformity of the inner ear. After that, many scholars reported a variety of congenital deformities of the inner ear, such as Mondini and Michel deformities, which are often quoted by later scholars, but are often misquoted. To make the description consistent, the author makes a brief review of it. Mondini convincingly demonstrated the zygomatic bone of an 8-year-old boy who was congenitally deaf and died of an accident