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目的:探讨磁共振评估肝脏铁过载方法的临床价值。方法:搜集49例β-重症地中海贫血患儿进行磁共振肝脏T2*及肝脏铁含量(LIC),以及血清铁蛋白的测定,并经过统计分析3者之间的相关性。结果:肝脏T2*检测49例患儿无铁过载2例(4.0%),轻度铁过载11例(22.4%),中度铁过载31例(63.2%),重度铁过载5例(10.2%)。肝脏LIC检测22例,轻中度铁过载6例(27.3%),重度铁过载16例(72.7%)。血清铁蛋白(SF)水平与肝脏T2*值示存在负相关(r=-0.493,P=0.000);SF水平与LIC示存在正相关(r=0.599,P=0.003)。结论:肝脏磁共振T2*及LIC检测均可以无创、准确评价重症地中海贫血铁过载,具有很好的临床应用价值。
Objective: To investigate the clinical value of MRI in assessing liver iron overload. Methods: Forty-nine children with β-thalassemia major were enrolled in this study. T2 * and liver iron content (LIC), and serum ferritin were measured. The correlations among the three groups were statistically analyzed. Results: Liver T2 * detected 49 cases of children with iron overload in 2 cases (4.0%), mild iron overload in 11 cases (22.4%), moderate iron overload in 31 cases (63.2%), severe iron overload in 5 cases (10.2% ). Liver LIC test in 22 cases, mild to moderate iron overload in 6 cases (27.3%), heavy iron overload in 16 cases (72.7%). There was a negative correlation between serum ferritin (SF) and liver T2 * value (r = -0.493, P = 0.000). There was a positive correlation between SF level and LIC (r = 0.599, P = 0.003). CONCLUSION: Magnetic resonance T2 * and LIC detection of liver can be noninvasive and accurately evaluate the iron overload of thalassemia major, which has a good clinical value.