原发性腹膜后肿瘤(primary retroperitoneal tumor,PRT)是一类发生于腹膜后腔、病理来源复杂的肿瘤性疾病。PRT可起源于腹膜后潜在间隙内的血管、肌肉、神经、脂肪和淋巴等结缔组织及胚胎残留组织[1-5]。PRT早期常无明显临床表现,病人就诊时往往肿瘤巨大或已侵犯周围重要脏器和腹腔重要血管,完整切除肿瘤,包括受累的脏器和血管,仍是目前治疗PRT的唯一有效方法,能有效 Primary retroperitoneal tumor (PRT) is a type of neoplastic disease that occurs in retroperitoneum with complicated pathological origin. PRT can originate from connective tissue such as blood vessels, muscles, nerves, lipids and lymphatic tissues and residual tissue of embryos in the retroperitoneal space [1-5]. PRT often no obvious clinical manifestations, patients often have a huge tumor or have been infiltrating the surrounding vital organs and abdominal vital vessels, complete resection of the tumor, including the affected organs and blood vessels, is still the treatment of PRT the only effective method, effective