先天性无阴道为双侧副中肾管发育不全的结果,几乎都合并无子宫或有始基子宫,极个别患者仍有发育正常的子宫,但卵巢一般正常。染色体核型为46XX,此类患者智力及体格发育正常,具有典型的女性第二性征和心理,除阴道缺失外,外阴结构正常。曾先后有2例患者入住我科,从而获取一些体会,现报告如下。 Congenital absence of both sides of the bilateral duct hypoplasia results, almost all without uterus or primordial uterus, very few patients still have normal uterus, but the normal ovary. Chromosomal karyotype 46XX, such patients with normal intelligence and physical development, with a typical secondary sexual characteristics of women and psychology, in addition to vaginal loss, the vulva structure is normal. There have been 2 patients admitted to our department, in order to obtain some experience, are as follows.