多发性神经纤维瘤(VRD)并有双侧听神经瘤患者的治疗问题非常棘手,其主要原因是肿瘤常侵犯耳蜗神经和耳蜗内,此外手术常影响长入肿瘤内的内听动脉枝,故用手术摘除肿瘤企图保存听力的希望很小。本组9例 VRD 其中7例肿瘤已长入耳蜗和螺旋神经节。因而作者提出对此病采用化疗,基于文献已成功地报道了用化疗治疗对生命有潜在危险的其它良 The treatment of patients with multiple neurofibromatosis (VRD) and bilateral acoustic neuroma is very difficult. The main reason is that the tumor often invades the cochlear nerve and the cochlea. In addition, the surgery often affects the internal auditory artery branches that grow into the tumor. There is little hope of surgical removal of the tumor in an attempt to preserve hearing. In this group of 9 cases of VRD, 7 cases of tumors have grown into the cochlea and spiral ganglion. Therefore, the author proposes to use chemotherapy for this disease. Based on the literature, it has successfully reported that other treatments are potentially hazardous to life with chemotherapy.