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承(雨留)病(Gargoylism)亦名Hurler氏综合征,或粘多糖代谢病I型。国内有关承(雨留)病报告不多,自1955年至1964年年底,共报告18例,(北京3例,浙江3例,上海8例;河北1例,广州3例)。1965年作者于本院发现一例,71-74年间发现四例,(其中两例为同胞姊妹,另两例为同胞兄弟),均具有典型症状与体征。现以第一例为重点,提出报告,以供临床
Gargoylism is also known as Hurler’s syndrome, or type 1 of the mucopolysaccharidosis. There were not many reports of inheritance (rain retention) in our country. From 1955 to the end of 1964, a total of 18 cases were reported (3 cases in Beijing, 3 cases in Zhejiang and 8 cases in Shanghai, 1 case in Hebei and 3 cases in Guangzhou). In 1965, the author found one case in our hospital, and among the 71-74 years, four cases were found (two of them were siblings and the other two were siblings) with typical symptoms and signs. The first case is now focused on the report for clinical use