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患儿,男性,13岁,初生后下肢及足背部发绀,生后2年,口唇出现发绀,呼吸、哭闹时明显.后逐渐加重。易感冒,喜蹲踞,缓慢步行时无胸闷、呼吸困难,急速行走后口唇紫绀加重。与同龄儿童相比其智力、体力、发育明显受限。患儿无咯血,无下肢浮肿。查体:T36.5℃,R21次/分,P82次/分,BP右上肢16/12kPa,左上肢16/12kPa,右下肢13/10kPa,左下肢14/8kPa。发育迟缓,营养差,神清语利,反应可。心前区无隆起,心尖搏动不明显,未触及震颤,心界不大,心率90次/2分,律齐,P_2亢进。四肢可见杵状指(趾),桡动脉、股动脉搏动尚可,腘动脉搏动弱,足背动脉扪及不清。辅助检查:血常规WBC5.6* 10~9/L、N0.69 L0.31,RBC 6.36* 10~(12)/L,
Children, men, 13 years old, after birth, lower extremities and dorsal foot cyanosis, 2 years after birth, lips appear cyanosis, breathing, crying when obvious. Gradually aggravated. Susceptible to cold, hi squat, slow chest without chest tightness, difficulty breathing, rapid walking cyanosis increased lips. Compared with children of the same age, their intelligence, physical strength and development are obviously limited. Children without hemoptysis, no lower limb edema. Examination: T36.5 ℃, R21 beats / min, P82 beats / min, BP right upper limb 16 / 12kPa, left upper limb 16 / 12kPa, right lower limb 13 / 10kPa, left lower limb 14 / 8kPa. Stunted, poor nutrition, clear language proficiency, the reaction can be. Pre-anterior region without uplift, apex beat is not obvious, did not touch the tremor, the heart is not big, heart rate 90 beats / 2 minutes, law Qi, P 2 hyperthyroidism. Extremities visible clubbing fingers (toe), radial artery, femoral artery pulse is still available, 腘 weak pulse, palpable dorsal artery palpable. Auxiliary examination: blood WBC5.6 * 10 ~ 9 / L, N0.69 L0.31, RBC 6.36 * 10 ~ (12) / L,