皮肌炎是以皮肤、肌肉及小血管炎症为特点的结缔组织病,其病因尚未明了。儿童皮肌炎为一种少见病,与成人皮肌炎比较,多见有肌萎缩、关节挛缩、胃肠受累、钙质沉着等;雷诺氏现象与伴发肿瘤在小儿甚为少见,而成人患者中10～20%可有之、近年来发病似有增多趋势,国内曾见30例儿童皮肌 Dermatomyositis is a connective tissue disease characterized by inflammation of the skin, muscles and small blood vessels, and its etiology is unknown. Children with dermatomyositis is a rare disease, compared with adult dermatomyositis, more common muscle atrophy, joint contracture, gastrointestinal involvement, calcifications, etc .; Raynaud’s phenomenon and associated with the tumor in children is very rare, and adults 10 to 20% of patients may have it, the incidence seems to increase in recent years, the trend has seen 30 cases of domestic children’s skin muscle