患者,男,23岁,以左髂部包块住院跛行,有外伤史,骨盆平行左髂骨8×7cm~2膨胀性破坏,以骨囊肿手术,术中见包块内大量陈旧性血块,术后出血不止,经输血、止血综合治疗出血控制。追问病史无遗传性家族病灾,化验凝血时间正常。经血液学检查证实为Ⅷ因子缺乏,本病最后诊为血友病甲型,左髂骨血友病性假肿瘤。 The patient, male, 23 years old, was hospitalized with a left temporal mass and had a history of trauma. The pelvis parallel left iliac bone was 8×7cm~2 expansively damaged. The operation was performed with a bone cyst. During the operation, a large number of old blood clots were seen in the mass. Hemorrhage does not stop after the operation. Hemorrhage is controlled by transfusion and hemostasis. No history of inherited family diseases was asked in the history, and the clotting time was normal. Hematological examination confirmed the absence of factor VIII. The final diagnosis of this disease was hemophilia type A and left iliac hemophilia pseudotumor.