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患儿女,9岁。出生后发现重度紫绀,临床诊断为复杂先天性心脏病:右心室双出口合并完全性房室隔缺损、肺动脉狭窄,右位心。分两期体外循环下行双向Glenn术和心内管道Fontan术,近期再次出现紫绀、运动耐量差。彩超显示:无脾脏,主动脉、下腔静脉分别位于脊柱右、左两侧;心尖指向右下,十字交叉结构消失,单心房,两个心室、左袢,共同房室瓣关闭不全,心房大、右室大,室间隔缺损位于双动脉下;两条大动脉均起自右室,主、肺动脉呈前后
Children with children, 9 years old. Severe cyanosis was found after birth, clinical diagnosis of complex congenital heart disease: double outlet right ventricle with complete atrioventricular septal defect, pulmonary stenosis, right centimeter. Two-phase cardiopulmonary bypass two-way Glenn surgery and intracardiac Fontan surgery, cyanosis again recently, poor exercise tolerance. Color Doppler ultrasound showed: no spleen, aorta, inferior vena cava were located in the right and left sides of the spine; apical pointing to the right, the cross-shaped structure disappeared, single heart, two ventricles, left lobe, common atrioventricular valve regurgitation, atrial , Right ventricular large, ventricular septal defect located in double arteries; two major arteries from the right ventricle, the main, pulmonary artery was before and after