论文部分内容阅读
体质性黄疸是由于肝细胞对胆红素代谢有先天性的缺欠,致使胆红素(间接型或直接型)在体内潴留,表现为长期持续的黄疸或是间歇反复发作性的黄疸。除黄疸以外,肝功能多正常。而且除其中的Grigler-Najjar氏综合征多伴有核黄疸之外,其他几型预后是良好的。体质性黄疸多是先天性家族性的表现。在本世纪初(1901年)Gilbert氏等以Cholemic simple fam-
Physical jaundice is due to liver cells have a congenital lack of bilirubin metabolism, resulting in bilirubin (indirect or direct type) retention in the body, manifested as long-term persistent jaundice or intermittent recurrent jaundice. In addition to jaundice, more than normal liver function. And in addition to the Grigler-Najjar’s syndrome in which more with nuclear jaundice, the other types of prognosis is good. More than constitutional jaundice is the manifestation of congenital familial. At the beginning of this century (1901) Gilbert’s and other Cholemic simple fam-