肾血管平滑肌脂肪瘤临床较少见,国内文献仅有少数病例报告。我院收治一例肾血管平滑肌脂肪瘤并发大出血现报告如下: 患儿女性、10岁。主诉:左上腹疼痛并包块三月。患儿于入院前三月觉左上腹部疼痛,呈持续性阵发性加剧,伴疲倦无力、食欲不振,身体渐瘦,嗜睡。在当地就诊时发现左上腹部包块,未确诊转我院。以左上腹部包块性质待查入普外科。既往无血尿、潮热、盗汗、外伤等病史。二胎,出生时为难产,胎头吸引,产后颅顶部血肿。三岁时面部鼻翼两旁出现皮脂腺 Renal angiomyolipoma is rare in clinical practice, and only a few cases have been reported in domestic literature. A case of renal angiomyolipoma complicated with massive hemorrhage was reported in our hospital as follows: The children were 10 years old. Chief complaint: Pain in the left upper quadrant and massage in March. The patient felt pain in the left upper abdomen three months before admission, and showed persistent paroxysmal intensification with fatigue, weakness, loss of appetite, thinning of the body, and lethargy. The left upper abdominal mass was found at the local clinic and was not diagnosed and transferred to our hospital. The nature of left upper abdominal mass is to be checked into general surgery. He had no previous history of hematuria, hot flashes, night sweats, and trauma. Second child, born at birth, fetal head attraction, postpartum cranial hematoma. Sebaceous glands appear on both sides of facial alar at the age of three