对骨髓增生异常综合征误诊为阵发性睡眠性血红蛋白尿1例分析如下。1病历摘要女,49岁。因阵发性酱油色尿14 a,间断右上腹痛3 a入院。患者14 a前出现酱油色尿,化验糖水试验弱阳性,酸溶血试验阴性,尿罗氏试验阳性,诊断为阵发性睡眠性血红蛋白尿(PNH),服强的松40 m g,1次/d,治疗1 a One case of misdiagnosis of myelodysplastic syndrome as paroxysmal nocturnal hemoglobinuria is as follows. 1 medical record summary female, 49 years old. Due to paroxysmal soy sauce color 14 a, intermittent right upper abdominal pain 3 a admission. Patients had soy sauce discoloration 14 days before the test of weak positive sugar water test, acid hemolysis test negative urine Roche test positive diagnosis of paroxysmal nocturnal hemoglobinuria (PNH), prednisone 40 mg, 1 / d, Treatment 1 a