家族性结肠息肉病(FPC)是一种少见的遗传性疾病。其好发于左半结肠,右半次之,但全大肠均可发病。其常在发病后20~30年发生恶变。治疗以全结肠切除为正确方法,现阶段任何欲保留暂时无病变结肠的侥幸心理都是错误的。只有全结肠切除,彻底刊除其发病的病理基础,才是保证手术后无复发的关键。 Familial colon polyposis (FPC) is a rare genetic disease. It occurs in the left colon, right half of the time, but the entire colon can be the disease. It often becomes malignant in 20-30 years after onset. The treatment of colonic resection is the correct method. At this stage, any chance to retain the temporary disease-free colon is wrong. Only complete resection of the colon to completely eliminate the pathological basis of its pathogenesis is the key to ensuring no recurrence after surgery.