病历摘要:4岁男孩,因反复肺炎、中耳炎、进行性淋巴腺肿及肝脾肿大于1977年4月入院。2岁时作过骨髓检查,为粒系统幼稚细胞增多。入院时表现苍白、瘀斑、全身淋巴腺肿及肝脾肿大(各在肋下5及10厘米),贫血(血色素9.8克),血小板减少(4万)及白细胞增多(15,000),分类计数发现:中性成熟粒细胞减少(10％),粒系统幼稚细胞增高(30％),很少的原始细胞(2％)及大量的不典型单核样细胞(40％)。骨穿及骨髓 Medical records summary: 4-year-old boy, due to repeated pneumonia, otitis media, progressive lymphadenopathy and hepatosplenomegaly admitted in April 1977. 2 years old made bone marrow examination for the granulocyte system naive cells increased. Symptoms were pale, ecchymosis, systemic lymphedema and hepatosplenomegaly (each 5 and 10 cm below the ribs), anemia (hemoglobin 9.8 grams), thrombocytopenia (40,000) and leukocytosis (15,000) Found: neutrophil neutropenia (10%), granulocyte system naive cells increased (30%), very few primitive cells (2%) and a large number of atypical mononuclear cells (40%). Bone wear and bone marrow