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目的探讨小儿膀胱横纹肌肉瘤(rhabdomyosarcoma,RMS)的影像表现。资料与方法对1例小儿膀胱RMS的临床及影像资料进行分析,并结合文献进行复习。结果患儿RMS位于膀胱颈及尿道内口,并沿尿道侵犯前列腺,肿块呈“葡萄簇”状,CT平扫密度均匀,低于腹壁肌肉,未见坏死及钙化,增强扫描肿块逐渐强化,边缘呈持续明显强化,邻近膀胱壁稍增厚。多平面重组(MPR)清晰显示肿块形态及侵犯范围。结论小儿膀胱RMS影像表现具有一定的特征性,结合患儿年龄及临床特征可做出正确诊断。
Objective To investigate the imaging manifestations of rhabdomyosarcoma (RMS) in children. Materials and Methods Clinical and imaging data of 1 case of infantile bladder RMS were analyzed and reviewed in combination with the literature. Results RMS was located in the bladder neck and urethral orifice, and along the urethra invade the prostate, the tumor was “grape cluster” shape, CT plain density, lower than the abdominal muscles, no necrosis and calcification, enhanced scan mass gradually strengthened , The edge was significantly enhanced, slightly thicker adjacent to the bladder wall. Multiplanar reorganization (MPR) clearly shows tumor morphology and extent of invasion. Conclusion The manifestations of children’s bladder RMS images have certain characteristics. Combined with the age and clinical features of children, correct diagnosis can be made.