目的：强调Ⅱ型神经纤维瘤病头部ＭＲＩ的诊断和增强扫描价值。材料与方法：搜集我院行ＭＲ检查并经手术证实符合神经纤维瘤病诊断标准者３例，分析其头部ＭＲＩ表现。结果：３例中２例为双侧听神经鞘瘤，其中１例伴有双侧三叉神经鞘瘤及脑膜瘤，另１例为单侧听神经鞘瘤伴有多发小的其他颅神经鞘瘤和脑膜瘤。结论：Ⅱ型神经纤维瘤病最常表现为三叉神经和听神经肿物，ＭＲ增强扫描对发现小的病变最为敏感。 OBJECTIVE: To emphasize the value of MRI in the diagnosis and enhancement of MRI in the head of type II neurofibromatosis. Materials and Methods: We collected 3 cases of neurofibromatosis diagnosed by MR examination of our hospital and confirmed by operation, and analyzed the MRI performance of the head. RESULTS: Two of the 3 cases were bilateral auditory nerve sheath tumors, of which 1 was associated with bilateral trigeminal schwannomas and meningioma, and the other was unilateral acoustic schwannoma with multiple small cranial nerve sheath tumors and meninges. tumor. Conclusion: Type II neurofibromatosis is most commonly manifested as trigeminal nerve and acoustic nerve mass. MR-enhanced scanning is most sensitive to small lesions.