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小舞蹈病作为风湿热的一种表现,部分病人急性期MRI显示的尾状核损伤,支持纹状体机能障碍是引起舞蹈病的原因。本文报道1例MRI显示永久性基底节损伤者。 患儿男性,3岁,突发右侧肢体不自主运动2天,其前无外伤史。CT示右侧尾状核低密度。入院后患儿烦燥,右侧肢体偶发舞蹈样运动,深反射减退。咽拭子培养有β溶血性A型琏球菌生长,抗“O”滴度200托德(正常<200);其他实验室检查正常。MRI示右侧尾状核与壳核异常信号伴肿胀。予青霉素治疗6天后舞蹈病减轻,2周后症状完全消失,神经学病学检查正常。病后3月MRI示尾状核与壳核肿胀消失,但该区仍有异常信号,病后22月和40月复查时,此种异常信号依然存在。
Small chorea as a manifestation of rheumatic fever, some patients showed acute caudate nucleus MRI damage, support for striatal dysfunction is the cause of chorea. This article reports 1 case of MRI showed permanent basal ganglia injury. Male children, 3 years old, involuntary movement of right limbs sudden 2 days, no previous history of trauma. CT shows the right caudate nucleus low density. Infantile irritability after admission, occasional dance on the right side of the body movement, deep reflexes. Throat swabs were incubated with beta-hemolytic B. anthracis with an anti-O titer of 200 Todd (normal <200); other laboratory tests were normal. MRI showed swelling of the right caudate and putamen signals. Cholera to 6 days after treatment to reduce chorea, 2 weeks after the symptoms completely disappeared, neurological examination was normal. After the disease in March MRI showed caudate and putamen swelling disappeared, but there are still abnormal signals in the area, the disease after review in 22 and 40, the abnormal signal still exists.