论文部分内容阅读
目的 :总结分析唾液腺淋巴上皮癌(lymphoepithelial carcinoma,LEC)的临床病理资料,为进一步提高诊治率提供参考。方法:对2006年1月—2016年9月诊治的15例LEC病例从流行病病因学、临床表现、诊断、治疗及预后等方面进行回顾性分析。结果:15例患者中,原发于腮腺8例,下颌下腺7例。男9例,女6例。发病年龄24~61岁,病程从20 d到10余年不等。患者中除1例来自黑龙江外,其他均来自中国南方。术后进行免疫组织化学检测,8例EB病毒原位杂交,阳检率为100%。术后随访13个月~10 a,除3例患者失访外,仅1例死亡,主要死亡原因为复发及转移。结论:唾液腺淋巴上皮癌是一种罕见的恶性肿瘤,颈淋巴转移率高。该病缺乏特征临床表现,需借助组织病理学检查予以确诊。治疗上首选根治性切除,手术无法彻底切除或淋巴结转移者术后辅助放疗,T3期及以上患者需辅助化疗。
OBJECTIVE: To summarize the clinical and pathological data of lymphoepithelial carcinoma (LEC) and provide references for further improving the diagnosis and treatment rate. Methods: Fifteen cases of LEC diagnosed and treated from January 2006 to September 2016 were retrospectively analyzed from the etiology, clinical manifestations, diagnosis, treatment and prognosis of the epidemic. Results: Of the 15 patients, 8 were parotid gland and 7 were submandibular gland. 9 males and 6 females. Age of onset of 24 to 61 years of age, duration from 20 d to more than 10 years. In addition to a patient from Heilongjiang, the others are from southern China. Postoperative immunohistochemical detection, 8 cases of Epstein-Barr virus in situ hybridization, the positive rate was 100%. All the patients were followed up for 13 months to 10 years. Except for 3 patients, only 1 patient died and the main cause of death was recurrence and metastasis. Conclusions: Salivary gland lymphoepithelial carcinoma is a rare malignant tumor with high rate of cervical lymph node metastasis. The lack of clinical features of the disease, need to be confirmed by histopathology. Radical resection of the treatment of choice, surgery can not be completely removed or lymph node metastasis postoperative adjuvant radiotherapy, T3 and above patients need adjuvant chemotherapy.