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镰状细胞贫血(SCA)仍是一种发病率及死亡率都高的疾病。治疗方法是预防血管闭塞及感染的发生。一旦这些情况发生,主要是症状性的。在其他严重的血红蛋白病中(如地中海贫血),骨髓移植(BMT)是有效的疗法,尽管对于该疗法的适应症仍有争论。现有一篇关于镰状细胞贫血患儿的报道。患儿因急性髓母细胞性贫血而施行骨髓移植。自1986年4月以来,已为5名严重的SCA患儿施行同种异体的骨髓移植。 5名患儿来自扎伊尔,均患重型镰状细胞性贫血,接受同种异体骨髓移植。选择这些病
Sickle-cell anemia (SCA) remains a disease with high morbidity and mortality. Treatment is to prevent vascular occlusion and infection. Once these conditions occur, mainly symptomatic. In other severe hemoglobinopathies (such as thalassemia), bone marrow transplantation (BMT) is an effective therapy, although the indications for this therapy are still debated. There is a report on children with sickle cell anemia. Children with acute myeloid leukemia and bone marrow transplantation. Since April 1986, allogeneic bone marrow transplantation has been performed in 5 severe SCA infants. Five children were from Zaire, both of whom had severe sickle cell anemia and underwent allogeneic bone marrow transplantation. Choose these diseases