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总结原发性肺肉瘤的诊断与治疗经验。对 8例原发性肺肉瘤病人进行了手术治疗。男性 3例 ,女性 5例 ;年龄在 14~ 6 8岁 ,平均 35.3岁。胸部X线及CT检查均显示肺内较大的肿块影 ,病变大小 5~ 12cm ,平均 7.9cm(>6cm ,87.5% )。所有病人入院时均被误诊。术前 1例平滑肌肉瘤病人通过肺穿刺确诊。8例病人手术中 7例根治 ,1例姑息切除 ;无手术死亡及术后并发症。总 5年生存率为 37.5% ,其中平滑肌肉瘤病人达 50 %。由于本病少见 ,与其他肺肿瘤有着类似的临床特征 ,故常被延误诊治 ,早期发现 ,早期手术切除并配合放疗可提高术后生存率
Summing up the diagnosis and treatment experience of primary pulmonary sarcoma. Eight patients with primary pulmonary sarcoma were treated surgically. There were 3 males and 5 females; the age ranged from 14 to 68, with an average of 35.3 years. Chest X-ray and CT examination showed large masses in the lungs. The lesion size was 5-12cm, with an average of 7.9cm (>6cm, 87.5%). All patients were misdiagnosed when they were admitted to hospital. One patient with leiomyosarcoma before surgery was confirmed by lung puncture. Eight patients underwent radical surgery in 7 cases, 1 palliative resection, and no operative death or postoperative complications. The overall 5-year survival rate was 37.5%, with 50% of leiomyosarcoma patients. Because this disease is rare and has similar clinical characteristics with other lung tumors, it is often delayed diagnosis and treatment. Early detection, early surgical resection combined with radiotherapy can improve the survival rate after surgery.