结节性硬化症(TSS)是临床上少见的一种神经系统的先天性疾病,以皮脂腺瘤、癫痫发作及痴呆为本病的三大特征。现将本院1985年6月至1987年2月收治的4例报告如下。典型病例例1:男,4岁。以发作性连续点头、四肢屈曲、两眼凝视近1年,经常发呆,有时多动、粗暴而入院。出生3个月开始发病。当时EEG:“高 Tuberous sclerosis (TSS) is a clinically uncommon neurological congenital disease characterized by sebaceous adenomas, seizures and dementia-based disease. Now our hospital from June 1985 to February 1987 admitted 4 cases are as follows. Typical case example 1: male, 4 years old. To nocturnal nodded, limb flexion, his eyes staring nearly 1 year, often in a daze, and sometimes move, rude and admitted to hospital. Three months after birth onset. EEG at the time: "high