乳头状胶质神经元肿瘤(papillary glioneuronal tumour,PGNT)是WHO(2007)中枢神经系统肿瘤分类中新增的实体肿瘤[1]。目前文献报道仅有38例,国内4例[2,3],十分罕见。本文报道1例PGNT,参照WHO(2007)神经系统肿瘤新分类,并复习相关文献,探讨该肿瘤的临床特点、影像学改变及组织学 Papillary glioneuronal tumor (PGNT) is a new solid tumor in the classification of the central nervous system tumors of WHO (2007) [1]. At present, there are only 38 cases reported in the literature and 4 cases in China [2,3]. It is very rare. This article reports a case of PGNT, with reference to WHO (2007) new classification of nervous system tumors, and review the literature to explore the clinical features of the tumor, imaging changes and histology