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Pelger-Huet白细胞异常自1928年首先由Pelger报告以后,国内外均有报道。现将我院1例遗传性Pelger-Huet氏白细胞异常及其家族34人调查情况报告于下。病例摘要患者男性、16岁,辽宁省盖县人,中学生。因间断发烧、肝脾淋巴结肿大、关节骨骼疼痛、反复皮疹1年,经3次住院,诊断为“免疫母细胞淋巴腺病”。患
Pelger-Huet leukocyte abnormalities were first reported by Pelger in 1928, both at home and abroad. Now one case of our hospital hereditary Pelger-Huet’s leucocyte abnormalities and 34 cases of family survey report below. Case Summary Male patients, aged 16, Gaixian, Liaoning Province middle school students. Due to intermittent fever, liver and spleen lymph nodes, joint pain, bone pain, repeated rashes 1 year, after 3 hospitalizations, diagnosed as “immunoblastic lymphocytic disease.” Suffering