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本征最早由Pohlins 于1740年报告。1952年Polhemus 归纳了本征的特点:先天无脾、内脏位置异常、心血管畸形。1955年Lve-mark’s 又作了详细描述故称Lvemark’s 综合征。本征少见且予后不良,尚无可靠治疗方法,大多数在婴儿期死亡。现将经病理检查证实的一例报告如下。患儿,男,1个月、住院号10218,足月顺产,第一胎第一产,本院接生,出生体重3.2Kg,娩后哭声强但皮肤青紫,哭叫时尤甚,入院前1天无诱因开始发热,但无咳喘,吮乳及尿、便均正常。父母身体健康,非近亲婚配,母孕期健康。查体:体温38.9℃、
The earliest was reported by Pohlins in 1740. 1952 Polhemus summarized the characteristics of the intrinsic: innate spleen, visceral location, cardiovascular malformations. 1955 Lve-mark’s made a detailed description of the so-called Lvemark’s syndrome. Intrinsic rare and poor prognosis, there is no reliable treatment, most died in infancy. Now confirmed by pathological examination of a case as follows. Children, male, 1 month, hospital number 10218, full-term follow-up, the first birth of the first birth, the hospital delivery, birth weight 3.2Kg, strong cries of skin after delivery, but bruising, especially crying, pre-admission 1 day no incentive to start fever, but no cough, sucking milk and urine, they are normal. Parents in good health, non-relatives of marriage, pregnant motherhood health. Physical examination: body temperature 38.9 ℃,