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目的探讨原发性腹膜后副神经节瘤的诊断和外科治疗方法。方法回顾性分析19例原发性腹膜后副神经节瘤患者的临床资料、诊断、治疗及预后。结果 15例患者有腹部包块、背部疼痛或双下肢水肿,其余4例无明显临床症状。术前均行CT检查,提示腹膜后占位性病变。均行手术治疗,复发7例,12例存活5年以上。结论原发性腹膜后副神经节瘤无特异性临床表现,术前定位诊断明确,定性诊断困难,手术是最佳治疗方案。
Objective To investigate the diagnosis and surgical treatment of primary retroperitoneal paraganglioma. Methods The clinical data, diagnosis, treatment and prognosis of 19 patients with primary retroperitoneal ganglioma were analyzed retrospectively. Results 15 patients had abdominal mass, back pain or both lower extremity edema, the remaining 4 patients without obvious clinical symptoms. Preoperative CT examination, suggesting that retroperitoneal space-occupying lesions. All patients underwent surgical treatment, with 7 cases relapsed and 12 cases surviving more than 5 years. Conclusion Primary retroperitoneal ganglioneuroma has no specific clinical manifestations, definite diagnosis of preoperative positioning, difficult diagnosis, and surgery are the best treatment options.