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Key FactsSynonyms:Congenital aural dysplasia,microtiaDefinition:Stenosis or atresia of external auditory canal(EAC)with associated auricle(external ear)deformity.May be isolated malformation,or part o f a cranial-facial syndrome,such as Crouzon’s,Goldenhar’s or Pierre Robin.Classic imaging appearance(CT):(1)Bony or membranous stenosis or atresia of EAC;(2)Underdeveloped mastoid air cells and small middle ear cavity;(3)Malformations of malleus and incus are common.
Key FactsSynonyms: Congenital aural dysplasia, microtiaDefinition: Stenosis or atresia of external auditory canal(EAC)with associated auricle(external ear)deformity.May be isolated malformation, or part ofa cranial-facial syndrome,such as Crouzon’s,Goldenhar’s or Pierre Robin. Classic imaging appearance (CT): (1) Bony or membranous stenosis or atresia of EAC; (2) Underdeveloped mastoid air cells and small middle ear cavity; (3) Malformations of malleus and incus are common.