目的探讨烟雾病(moyamoya disease,MMD)的临床特点及DSA表现。资料与方法15例患者经DSA诊断为MMD,分析其临床特点及DSA表现,并与CT资料对比分析。结果CT示脑出血11例(其中原发脑室出血6例),脑梗死3例,1例正常;DSA示双侧病变14例,单侧病变1例。所有病例均见颅底及基底节区异常增生血管网及颈内、外动脉侧支循环建立。结论对于反复出现脑缺血症状或CT提示原发性脑室出血、脑叶或颅底多发出血或梗死灶的中青年患者应考虑MMD可能,DSA可确诊MMD,并对侧支循环的评价具有独特的优势。 Objective To investigate the clinical features and DSA manifestations of moyamoya disease (MMD). Materials and Methods Fifteen patients were diagnosed as MMD by DSA. The clinical features and DSA findings were analyzed and compared with CT data. Results CT showed cerebral hemorrhage in 11 cases (including 6 cases of primary ventricular hemorrhage), cerebral infarction in 3 cases, 1 case of normal; DSA showed bilateral lesions in 14 cases, unilateral lesions in 1 case. All cases were found in the basal ganglia and basal ganglia dysplasia and internal carotid artery, external artery collateral circulation established. Conclusions MMD may be considered in middle-aged and young patients with recurrent cerebral ischemia or CT suggestive of primary intraventricular hemorrhage and multiple hemorrhage or infarction in lobar or basal skull. DSA can confirm MMD and has a unique The advantages.