肠病性肢端皮炎(Acrodermatitisenteropathica,简称AE)属常染色体隐性遗传性疾病。临床表现为躯体孔口周围皮损、顽固性腹泻、毛发脱落三大主要症状。1942年Daubott首先对本病命名,并认为与锌代谢紊乱有关,直至1973年Moynohan等用锌治疗以来,才引起重视。我们最近遇到2例,报告如下。 Acrodermatitisenteropathic (AE) is an autosomal recessive disease. Clinical manifestations of the skin around the orifice, intractable diarrhea, hair loss three major symptoms. Daubott first named the disease in 1942 and considered it to be linked to a disorder of zinc metabolism that was not recognized until 1973 when Moynohan et al treated it with zinc. We recently encountered two cases, the report is as follows.