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80%慢性自身免疫性血小板减少性紫癜(ATP) 患者,在类固醇治疗或脾摘除术后,血小板数可达正常,但某些病例仍有持续出血。为此,作者研究了49例ATP患者(男性18人,女性31人,年龄5-63岁),并以49名正常人为对照。病人均无脾肿大,骨髓中巨核细胞数正常或增加,排除了其他原因所致的血小板减少。作者测定病人的血小板数、巨血小板(直径大于3μm)百分数,血小板相关IgG值(PAIgG)及血小板功能试验,包括:出血时间、血小板聚集试验、内源性血清素量、血小板和血浆β-血小板球蛋白(β-
In 80% of patients with chronic autoimmune thrombocytopenic purpura (ATP), platelets are up to normal after steroid treatment or splenic extirpation, but persistent bleeding remains in some cases. To this end, the authors studied 49 cases of ATP patients (18 males, 31 females, aged 5-63 years), and 49 normal controls. No splenomegaly in patients with normal or increased number of bone marrow megakaryocytes, ruled out other causes of thrombocytopenia. The authors measured platelet counts, percentages of platelets (> 3 μm in diameter), platelet-associated IgG values (PAIgG), and platelet function tests including bleeding time, platelet aggregation assay, endogenous serotonin levels, platelets and plasma β-platelets Globulin (β-