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目的研究探讨髓内高分化骨肉瘤的临床病理特点及鉴别诊断。方法通过光镜及免疫组化方法研究1例髓内高分化骨肉瘤。该患者复发了2次,最终转移到T12椎体,随访8年。结果1例28岁女性患者,1998年在左股骨远端患髓内高分化骨肉瘤。2002年和2003年复发2次,2004年转移到T12椎体,呈低分化肉瘤样变。结论髓内高分化骨肉瘤常多发生于中、青年,早期诊断较困难,了解其病理、免疫组化特点及鉴别诊断,结合临床及X线表现,将有助于做出正确的诊断。
Objective To investigate the clinicopathological features and differential diagnosis of intramedullary well-differentiated osteosarcoma. Methods One case of intramedullary well-differentiated osteosarcoma was studied by light microscopy and immunohistochemistry. The patient relapsed 2 times, and eventually transferred to the T12 vertebral body, followed up for 8 years. Results A 28-year-old woman with intramedullary well-differentiated osteosarcoma at the distal femur of the left femur in 1998. Two recurrences in 2002 and 2003, 2004 T12 vertebral body was transferred, showed poorly differentiated sarcomatoid. Conclusions Intramedullary well-differentiated osteosarcoma often occurs in young and middle-aged patients. Early diagnosis is difficult. To understand its pathological features, immunohistochemical features and differential diagnosis, combined with clinical and X-ray findings, will help to make a correct diagnosis.