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真性红细胞增多症系以红细胞增多为特征的克隆源性慢性骨髓增殖性疾病,然而有关红系或其增殖能力方面的量化标准则报道甚少。体外研究业已揭示本病红系祖细胞在各种培养体系均能自发分化、生长,它们对促红细胞生成素异常敏感,所需甚微;而继发性改变及正常人骨髓细胞培养不加促红细胞生成素,合成血红蛋白的细胞克隆则不能形成。作者对28例真性,20例继发性红细胞增多症及15
Polycythemia vera is a clonogenic chronic myeloproliferative disorder characterized by an increase in polycythemia, however, little is known about the quantitative criteria for erythroid or its proliferative capacity. In vitro studies have revealed that this disease erythroid progenitor cells in various culture systems can spontaneous differentiation, growth, they are sensitive to the exception of erythropoietin, the required little; and secondary changes and normal human bone marrow cell culture without the promotion Erythropoietin, cell clones that synthesize hemoglobin do not form. The authors of 28 cases of true, 20 cases of secondary polycythemia and 15