烟雾病为原因不明的颅底动脉进行性狭窄以致闭塞的疾病。由一侧颈内动脉发展到双侧颈内动脉,先影响颅底动脉环的前半部,后影响其后半部,最终造成颅底动脉环的全部闭塞。病程中伴有脑底异常血管网的形成及颅内、外吻合血管的建立。临床上儿 Moyamoya disease is an unexplained skull base artery occlusive disease. From one side of the internal carotid artery to the bilateral internal carotid artery, first affecting the first half of the skull base artery ring, after affecting the latter half, eventually resulting in complete occlusion of the skull base artery rings. The course of the disease accompanied by the formation of abnormal cerebral vascular network and intracranial and external anastomosis of blood vessels. Clinical children