本文报道一例特发性右心扩大并结合国内外文献对其病因、发病特点、临床表现、诊断、治疗及预后进行全面讨论。本病并非罕见，但确诊率极低。若能早期诊断，治疗，进行随访监护，减少及预防致命性心律失常及心衰发生，预防猝死，是治疗的关键。 This article reports a case of idiopathic right heart enlargement combined with domestic and foreign literature on the etiology, incidence characteristics, clinical manifestations, diagnosis, treatment and prognosis of a comprehensive discussion. The disease is not uncommon, but the diagnosis rate is very low. If the early diagnosis and treatment, follow-up monitoring, reduce and prevent fatal arrhythmias and heart failure, prevent sudden death, is the key to treatment.