遗传性肾炎又名Ａｌｐｏｒｔ综合症，血尿为本病最为突出表现，并常为首发症状，蛋白尿一般不重，肾病综合征很少发生［１］；现报告以肾病综合征为主要临床表现的遗传性肾炎１例。病例男性，６岁半，以反复浮肿、蛋白尿４年入院，从１岁开始生长发育缓慢，面色始终苍黄，... Hereditary nephritis, also known as Alport syndrome, the most prominent manifestation of hematuria-based disease, and often the first symptom, proteinuria is generally not heavy, nephrotic syndrome rarely occurs [1]; the report is nephrotic syndrome as the main clinical manifestations One case of hereditary nephritis. Case of male, 6 years and a half to repeated edema, proteinuria 4 years admitted to hospital, from 1 year old growth and development slow, always yellowish, ...