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目的提高对致心律失常性右室心肌病的诊断、治疗及预后的认识,并提出今后课题。方法回顾性分析致心律失常性右室心肌病者的临床资料及随访结果。结果以室性心律失常起病常见,心电图、心脏彩超为主要诊断方法,治疗可选择药物、介入或手术,预后不佳。结论致心律失常性右室心肌病临床、心电图有一定特征,心脏彩超为主要诊断方法,目前尚未有哪一种治疗手段显示其优越性,较多问题有待今后探讨。
Objective To raise awareness of the diagnosis, treatment and prognosis of arrhythmogenic right ventricular cardiomyopathy and to propose future topics. Methods The clinical data and follow-up results of patients with arrhythmogenic right ventricular cardiomyopathy were analyzed retrospectively. Results The onset of ventricular arrhythmia common ECG, cardiac ultrasound as the main diagnostic methods, the treatment of choice of drugs, intervention or surgery, the prognosis is poor. Conclusions The clinical and electrocardiographic findings of arrhythmogenic right ventricular cardiomyopathy have some characteristics. Cardiac ultrasonography is the main diagnostic method. At present, there is not any kind of treatment that shows its superiority and more problems to be explored in the future.