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为探讨外生性面神经雪旺氏细胞瘤的病理来源及病因 ,对 152 6耳颞骨连续切片进行组织病理学观察。结果发现 :39耳在面神经骨性管裂处显示神经外膜先天性缺损 ,神经主干由此疝出。其中31耳 ,在疝出面神经凸面有明显的雪旺氏细胞增生。这 31耳中 ,有 12耳在卵圆窗上方 ,1耳在面神经第二膝部形成小的外生性雪旺氏细胞瘤。提示 :管裂处神经外膜的先天性缺损是面神经由此疝出的组织解剖学原因。面神经疝出可能是刺激雪旺氏细胞增生 ,以致形成外生性面神经雪旺氏细胞瘤的直接原因。
In order to investigate the pathogenic origin and etiology of exogenous facial nerve Schwann cell tumor, 152 6 consecutive sections of the ear temporal bone were observed histopathologically. The results showed that: 39 ears in the facial nerve bony rupture of the epicardial congenital defect, the nerve trunk from hernia. Of which 31 ears, herniated facial convex obvious Schwann cell proliferation. Of the 31 ears, 12 ears were above the oval window and 1 ear formed a small exogenous Schwannoma tumor in the second knee of the facial nerve. Hint: The congenital defect of the neuro-epicardial canal is the anatomic cause of the herniation of the facial nerve. Facial herniation may be stimulated Schwann cell proliferation, resulting in the formation of exogenous facial nerve Schwannoma directly cause.