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本文描述了6例恶性(急性)骨髓硬化/纤维化(MMS)患者的临床及形态学发现。根据Lewis等的定义,MMS具有下列症状:全血细胞减少,循环红细胞有轻度(或无)异常,末梢血中原始细胞增多,显示有各系列幼稚细胞的骨髓纤维化,无肝脾肿大,特征性的迅速致死的病程。本文6例完全符合上述MMS的临床标准,而且还有充分的血液学资料及详尽的细胞病理学检查,以使诊断更确实。6例中5例
This article describes the clinical and morphological findings of 6 patients with malignant (acute) myelo sclerosis / fibrosis (MMS). According to the definition by Lewis et al., MMS has the following symptoms: pancytopenia, mild (or no) abnormalities of circulating red blood cells, increased priming cells in peripheral blood, myelofibrosis of various series of naive cells, no hepatosplenomegaly, Characteristic rapid death process. This article 6 cases fully meet the clinical criteria of MMS, but also have adequate hematological data and detailed cytopathological examination, so that the diagnosis is more accurate. 6 cases in 5 cases