单心室是一种少见的复杂的先天性心脏畸形,即左右心室之间无室间隔存在,其共同心室接受左右房室瓣或共同房室瓣的血流。单心室从解剖上可分为四种基本类型:A型为单纯左室无右室窦部;B型为单纯右室无左室窦部;C型为原始室间隔缺如或仅有室间隔残迹;D型则无两心室窦部(体部)。上述四类按其大动脉的关系又可分为三种亚型:I型为大动脉位置正常,Ⅱ型为右位型大动脉错位(主动脉瓣位于肺动脉瓣的右前侧),Ⅲ型为左位型 Single ventricle is a rare and complex congenital heart malformation, that is, there is no ventricular septum between the left and right ventricular presence, its common ventricle to accept the left atrial or common atrioventricular valve blood flow. Single ventricle from the anatomy can be divided into four basic types: A type of simple left ventricular sinus without right ventricle; B-type simple right ventricle without left ventricular sinus; C type of the original ventricular septal defect or only ventricular septum Remnants; D-type no two-ventricle sinus (body). The above four categories according to the relationship between the major artery can be divided into three subtypes: type I for the location of the aorta, type for the right type of major artery dislocation (aortic valve located in the right anterior pulmonary valve), type Ⅲ for the left type