进行性肌营养不良症是一种遗传家族性疾病。常累及心肌并发心肌病。我们观察同一家族4例肌营养不良患者中2例并发心肌病的心电图改变。现报告如下,并参考有关文献略加讨论。病例摘要例一,男,34岁,住院号14077。自5～6岁开始四肢肌肉萎缩、无力、行走不便.至入院前一个月有心悸、气急、腹胀、尿少于1977年9月9日入院。家族史(见家系调查)。体检:T36℃,p80次/分,Bp110/80mmHg。面、唇、指端紫绀。颈静脉怒张,两肺底有湿罗音。心界扩大,心律不规则,心关部Ⅱ级收缩期杂音和Ⅱ级舒张期杂音,P_2>A_2。腹部膨隆,肝肋下2cm,质中,有触痛,肝颈返流征(+),脾未及,腹水征(+)。腰椎向左侧弯,翼状肩肿,四肢肌肉萎缩,以近 Progressive muscular dystrophy is a hereditary familial disease. Often involving the myocardium and cardiomyopathy. We observed changes in the electrocardiogram of 2 patients with cardiomyopathy in 4 patients with muscular dystrophy in the same family. Now report as follows, and with reference to the literature a little discussion. A case summary, male, 34 years old, hospital number 14077. From 5 to 6 years old limbs muscle atrophy, weakness, walking inconvenience to a month before admission palpitations, shortness of breath, abdominal distension, less urine than September 9, 1977 admission. Family history (see family survey). Physical examination: T36 ℃, p80 times / min, Bp110 / 80mmHg. Face, lips, fingers cyanotic. Jugular vein engorgement, both ends of the lung wet rales. Heart widening, irregular heart rhythm, cardiac level Ⅱ systolic murmur and diastolic murmur, P_2> A_2. Abdominal bulging, liver ribs 2cm, quality, tenderness, liver reflux syndrome (+), spleen and ascites (+). Lumbar bending to the left, wing-shaped shoulder swollen limbs muscle atrophy to