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目的:总结1例诊断颅底异常血管网病飞行人员的临床过程。方法:对空军特色医学中心诊断治疗的1例颅底异常血管网病飞行人员的临床资料进行报道,并文献分析。结果:本例患者为男性领航员,41岁。主要表现为高原驻训时易出现头昏不适,且耐缺氧能力差。脑血管造影证实该飞行人员存在颅底异常血管网病。脑血流灌注检查进一步证实其颅底异常血管网形成同侧脑血流减少。航空医学鉴定结论:飞行合格结论;健康等级:乙级。结论:颅底异常血管网病临床症状不典型,可无梗死灶,容易被漏诊。应根据飞行员的临床症状,重视其脑血灌注检查。“,”Objective:To summarize the diagnosis of a flying personnel with moyamoya disease.Methods:The clinical features of an aircrew with moyamoya disease which diagnosed in Air Force Medical Center were summarized and analyzed. Furthermore, the related literatures were reviewed.Results:The patient is a of 41-year-old male navigator. The Navigator usually felt dizzy in the training on the plateau. Also, his anti-anoxia ability was relatively weak. Digital subtraction angiography (DSA) showed the navigator was suffered from the moyamoya disease. Cerebral blood perfusion examination further confirmed moyamoya disease and indicated ipsilateral cerebral blood flow reduction. The conclusion of aviation medicine evaluation was flying qualification, and health level was class B.Conclusions:In most cases, the clinical symptoms of moyamoya disease are usually insignificant, and may not have cerebral infarction. So it’s easy to result in missed diagnosis. Therefore, more attention should be paid on aircrew’s cerebral blood perfusion examination upon his/her clinical symptoms.