强直性肌营养不良症是进行性发展的全身性疾病,特征为骨骼肌萎缩伴肌紧张。已证实本病有各种ECG异常表现,包括P波低平,房颤、房扑、Ⅰ、Ⅱ、Ⅲ度AV阻滞、室内传导阻滞、电轴左偏、左右束支阻滞、ST—T异常,室性早搏。电生理检查有A—H、H—V间期延长、希氏束分裂等。在英国文献中尚 Myotonic dystrophy is a progressive systemic disease characterized by skeletal muscle atrophy with muscle tension. Has confirmed that the disease has a variety of ECG abnormalities, including P wave low level, atrial fibrillation, atrial flutter, Ⅰ, Ⅱ, Ⅲ degree AV block, conduction block, left axis deviation, left and right bundle branch block, ST -T abnormal, premature ventricular contractions. Electrophysiological examination with A-H, H-V prolongation, His bundle splitting. In the British literature is still