成涎细胞瘤为发生于大唾液腺的先天性肿瘤,临床罕见,主要发生在腮腺,极少数发生在下颌下腺。由于其临床特点和影像学表现缺乏特异性,正确诊断常较困难。该肿瘤有局部浸润、侵袭和复发甚至淋巴结扩散和远处转移的可能,但淋巴结及远处转移较少发生,故治疗方法一般为手术完整切除,很少采用放化疗。儿童期且局限的成涎细胞瘤预后一般较好。本文报告1例腮腺成涎细胞瘤病例,并结合文献对其临床和病理特点、诊断、治疗及预后等进行讨论。 Salivary sarcoma is a congenital tumor occurring in the large salivary glands, which is rare in clinical practice. It mainly occurs in the parotid gland, and very few in the submandibular gland. Due to the lack of specificity of its clinical features and imaging findings, the correct diagnosis is often more difficult. The tumor has local infiltration, invasion and recurrence and even the possibility of lymph node dissemination and distant metastasis, but less frequent lymph node and distant metastasis, so the treatment is generally complete resection of the surgery, the use of radiotherapy and chemotherapy rarely. Childhood and confined into the salivary gland tumor prognosis is generally better. This article reports 1 case of parotid glioblastoma, combined with the literature on its clinical and pathological features, diagnosis, treatment and prognosis were discussed.