先天性脑肿瘤是指出生后两个月内发现的肿瘤。本病罕见,仅占儿科肿瘤的0.5～1.9%。作者回顾45例经病理证实的先天性脑肿瘤。做过CT的24例,MR 5例,超声6例,血管造影7例。2/3的病变位于幕上(31/45)。组织学上最常见的是原始或分化差的组织构成的肿瘤:畸胎瘤(12例)和原始神经外胚层肿瘤(12例),其中4例为典型的髓母细胞瘤。另外还有9例星形细胞瘤(Ⅰ～Ⅲ级);4 Congenital brain tumor is a tumor found within two months after birth. The disease is rare, accounting for only 0.5 to 1.9% of pediatric tumors. The authors review 45 cases of pathologically confirmed congenital brain tumors. CT done in 24 cases, MR 5 cases, 6 cases of ultrasound, angiography in 7 cases. Two-thirds of the lesions were on the screen (31/45). Histologically, tumors of primitive or poorly differentiated tissue were the most common tumors: teratoma (12 cases) and primitive neuroectodermal tumors (12 cases), of which 4 were typical medulloblastomas. In addition there are 9 cases of astrocytoma (Ⅰ ~ Ⅲ grade); 4