出血性疾病占血液系统疾病的三分之一。其特征为:自幼自发性出血或轻微损伤后反复广泛出血不止,止血效果差,多有家族史,出血原因为:(1)血管壁的功能障碍;(2)血小板数量或/和质的改变;(3)凝血因子的缺乏以及抗凝物质的增加等。诊断与鉴别诊断一、病史:病史是鉴别出血性疾病的首要步骤,因此,必须详细而完整地询问出血的病 Hemorrhagic disease accounts for one-third of all hematological disorders. It is characterized by repeated extensive bleeding after spontaneous bleeding or minor injury since childhood, poor hemostatic effect and many family history. The causes of bleeding are: (1) dysfunction of vessel wall; (2) number and / or quality of platelets Change; (3) the lack of clotting factor and the increase of anticoagulant substances. Diagnosis and differential diagnosis First, medical history: medical history is the first step to identify hemorrhagic disease, therefore, must be detailed and complete examination of bleeding disease