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中国出生缺陷监测网 1987~ 1992年以医院为基础在全国对孕 2 8w至产后 7d的围产儿进行监测 ,对30 0例先天性小肠闭锁或狭窄病例进行流行病学分析。结果表明 :我国先天性小肠闭锁或狭窄发生率为 0 .6 9/万 ,与国外一些国家的发生率近似。城乡发生率、男女发生率均无显著性差异。先天性小肠闭锁或狭窄是一种单发频率较高的畸形 ,单纯性先天性小肠闭锁或狭窄围产期病死率为 5 15‰ ,且围产期病死率随伴发畸形的增加而增加。本调查分析显示 :先天性小肠闭锁或狭窄是一种常见畸形 ,其患儿的存活率随着诊断和治疗水平的提高而提高。
China Birth Defect Monitoring Network From 1987 to 1992, based on the hospital, we monitored the perinatal children in the whole country from 28w to 7d postpartum, and conducted epidemiological analysis on 30 cases of congenital small intestinal atresia or stenosis. The results showed that: the incidence of congenital small intestinal atresia or stenosis was 0.69 million, similar to the incidence in some foreign countries. The incidence of urban and rural areas, the incidence of men and women no significant difference. Congenital intestinal atresia or stenosis is a single high frequency of deformity, simple congenital intestinal atresia or stricture perinatal mortality was 5 15 ‰, and perinatal mortality increased with the increase of accompanying deformity. The survey showed: congenital small bowel or atresia is a common deformity, the survival rate of children with diagnosis and treatment increased.