发生于涎腺的各种向皮脂腺分化的良、恶性肿瘤较为常见,但伴毛囊分化的涎腺肿瘤却非常罕见,其主要为毛母质瘤及毛母质癌,不仅患者的临床表现无特异性,而且肿瘤的病理学形态多样,需与多种其他肿瘤相鉴别,肿瘤的良、恶性亦很难确定,常易误诊。本文着重对其临床病理学特点、病理诊断和鉴别诊断、治疗原则及患者的预后等进行综述。 Salivary glands occur in a variety of sebaceous glands differentiate benign and malignant tumors are more common, but with salivary gland differentiation of hair follicles is very rare tumor, which is mainly hairy tumors and hairy tumor, not only the patient’s clinical manifestations of non-specific, And the pathological morphology of the tumor varied, with a variety of other tumors to be differentiated, benign and malignant tumors are also difficult to determine, often misdiagnosed. This article focuses on its clinical and pathological features, pathological diagnosis and differential diagnosis, treatment principles and prognosis of patients were reviewed.