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目的探讨口腔颌面部淋巴管畸形的临床特征与治疗方法,为临床积累经验,提高治疗效果。方法回顾性分析新疆医科大学第一附属医院口腔颌面外科2003年1月~2007年12月收治的110例口腔颌面部淋巴管畸形患者的临床资料。结果口腔颌面部淋巴管畸形共110例,男女性别之比为1.34∶1。发病年龄<1岁者为64例,占58.18%,<2岁者为76例,占69.09%。发生的部位依次为舌部(40.00%)、唇颊部(18.18%)、颈部(12.73%)及下颌下区、腮腺区。组织分型为微囊型72例,大囊型38例。手术治疗84例,占76.36%,平阳霉素局部注射13例,占11.82%,20%高渗盐水局部注射8例,占7.27%,手术+平阳霉素局部注射5例,占4.55%。结论口腔颌面部淋巴管畸形中,男性多于女性,小儿多见,好发部位依次为舌、唇颊部、颈部等。组织学分型以微囊型多见,大囊型相对少。手术切除、平阳霉素局部注射是治疗口腔颌面部淋巴管畸形的理想和有效手段。
Objective To investigate the clinical features and treatment of lymphatic malformations in oral and maxillofacial region, to accumulate clinical experience and improve the therapeutic effect. Methods The clinical data of 110 patients with oral and maxillofacial lymphangitic deformity who underwent oral and maxillofacial surgery in the First Affiliated Hospital of Xinjiang Medical University from January 2003 to December 2007 were retrospectively analyzed. Results A total of 110 cases of oral and maxillofacial lymphatic malformations were found. The ratio of male to female was 1.34:1. Age of onset <1 year was 64 cases, accounting for 58.18%, <2 years of age was 76 cases, accounting for 69.09%. Occurred in the order of the tongue (40.00%), lip and cheek (18.18%), neck (12.73%) and submandibular area, parotid gland area. Tissue typing for the microcapsule 72 cases, 38 cases of large capsule. Surgical treatment of 84 cases, accounting for 76.36%, Pingyangmycin local injection of 13 cases, accounting for 11.82%, 20% hypertonic saline local injection in 8 cases, accounting for 7.27%, surgery + Pingyangmycin injection in 5 cases, accounting for 4.55%. Conclusions In lymphatic malformations of oral and maxillofacial region, there are more males than females, more common in children. The predilection sites are tongue, lip and cheek, neck and so on. Histological type is more common in microcapsules, relatively less in large cysts. Surgical resection, local injection of pingyangmycin is an ideal and effective means for the treatment of lymphatic malformations in oral and maxillofacial region.