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我院眼科十余年来在一百多例单侧眼球突出症患者中证实6例为眶内神经纤维瘤,其中3例曾进行手术治疗,兹报告于下。临床资料:本组男性2例,女性4例。年龄16~30岁。入院视力:光感1例,眼前手动2例,≤0.13例,6例均有眼球突出,突出度最大者14mm。均为从小发病,逐年加重,上下睑有橡皮肿样增厚。眼眶X光片:眼眶扩大及不同程度的眶壁骨缺损和邻近骨受压。4例有全身皮肤散在神经纤维瘤和色素斑。手术情况:3例手术,1例麻醉时发生休克,经抢救脱险未手术。1例施行Kronlien—Berke外侧眶壁凿开术,剥离肿物至眶尖时出血不能控制,经压迫及大量输血止血,瘤组织软性无明显被膜,血管丰富,边界不清,难以彻底切除,取出肿物3.5cm×3.0cm×2.5cm,病理报告为神经纤维瘤。1例仅做部分切除活检,病理报告为丛状神经纤维瘤。
More than 10 years of ophthalmology in our hospital in more than one hundred cases of unilateral eyeball protrusion in patients with confirmed 6 cases of orbital nerve fibroids, of which 3 cases had surgery, it is reported below. Clinical data: The group of 2 males and 4 females. Age 16 to 30 years old. Admission vision: light perception in 1 case, the immediate manual in 2 cases, ≤ 0.13 cases, 6 cases were prominent in the eye, the largest degree of highlight 14mm. Are from a small incidence, increasing year by year, upper and lower eyelid with a swollen like. Orbital X-ray: orbital enlargement and varying degrees of orbital bone defects and adjacent bone compression. 4 cases of systemic skin scattered in neurofibromas and pigmented spots. Surgery: 3 cases of surgery, 1 case of shock occurred when anesthesia, after rescue without surgery. 1 case of Kronlien-Berke lateral orbital wall surgery, stripping the tumor to the orbital apex bleeding can not be controlled by the oppression and a large number of transfusion to stop bleeding, soft tissue tumor was not obvious, rich in blood vessels, the boundary is unclear, it is difficult to completely remove, Remove the tumor 3.5cm × 3.0cm × 2.5cm, the pathological report of neurofibroma. One case was only partial resection biopsy, pathology report for plexiform neurofibroma.