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目的:探讨卵睾性性发育疾病的特点及诊治方法。方法:对我院2011年来诊治的2例青春期卵睾性性发育疾病病例的诊治过程进行回顾性分析与总结。对患者进行系统的体格检查、染色体核型检查、性激素测定、腹部-盆腔-肾上腺彩超、尿道膀胱镜检查、h CG试验,充分的术前准备之后,在全麻下行腹腔镜下性腺探查与决定性别的性腺切除术及外阴矫形术。术中探查及病理证实2例患者双侧性腺均为卵睾,性别选择均为女性,1例行卵睾切除、1例切除睾丸组织,保留卵巢组织。结果:术后随访1年,2例患者外阴形态正常,生殖腺未见异常。结论:性腺探查是卵睾性性发育疾病诊断的唯一依据,性别选择是治疗的关键。腹腔镜下性腺探查及选择性切除术是首选方法。
Objective: To explore the characteristics of oviduct developmental diseases and diagnosis and treatment methods. Methods: The diagnosis and treatment of 2 cases of adolescent ooplasmosis in our hospital in 2011 were retrospectively analyzed and summarized. Patients underwent systematic physical examination, chromosomal karyotyping, sex hormone tests, abdominal-pelvic-adrenal ultrasound, urethral cystoscopy, hCG tests, adequate preoperative preparation, and laparoscopic gonad probing and decision under general anesthesia Sex gonadotomy and vulva orthopedics. Intraoperative exploration and pathology confirmed 2 cases of bilateral gonads are egg test, sex selection are female, 1 case of egg testis, 1 case of excision of testicular tissue, retained ovarian tissue. Results: All the patients were followed up for 1 year. The vulva morphology was normal in 2 patients and no abnormalities in gonads were observed. Conclusions: Sexual gland exploration is the only basis for the diagnosis of egg-testis developmental disease. Sex selection is the key to treatment. Laparoscopic gonad exploration and selective resection is the preferred method.